| CASE REPORT |
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| Year : 2015 | Volume
: 8
| Issue : 1 | Page : 39-41 |
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A neglected case of Klippel Trenaunay Weber syndrome
Vikram Khanna1, Gaurav Singh2, Sanjeev Kumar1, Sudhir Singh1
1 Department of Orthopaedics, Era's Lucknow Medical College, Lucknow, Uttar Pradesh, India
2 Department of Radiology, Era's Lucknow Medical College, Lucknow, Uttar Pradesh, India
Correspondence Address:
Vikram Khanna
Ranjana Hospital, 13, D-Road, Allahabad - 211 003, Uttar Pradesh
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/0975-7341.183958
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This congenital vascular disorder is described by a “triad” of symptoms affecting one or more limbs. The “triad” constitutes varicose veins, cutaneous hemangioma, with bone and soft tissue hypertrophy. The cutaneous hemangioma presents as a substantial port-wine stain or nevus. Varicose veins are often very numerous. Bone and soft tissue hypertrophy is variable in presentation and the affected limb may be either larger or smaller than the normal limb. This disorder is generally reported in childhood or adolescent age groups. We herein present a neglected case of Klippel Trenaunay Syndrome with all the classical clinical and radiological findings. A 30-year-old man reported with the classical triad. On clinical examination substantial port wine stain was seen and radiographs showed multiple bony outgrowths whereas MRI showed multiple varicosities displaying heterogeneous hyper intense signals on T2 Weighted Images and T1 hypo intensity with hypertrophy of soft tissue in left lower limb. |
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